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KMID : 0359020080370050384
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Korean Journal of Gastrointestinal Endoscopy
2008 Volume.37 No. 5 p.384 ~ p.388
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A Case of Pancreatic Dual Wirsung Ducts in a Patient with von Hippel-Lindau Disease
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Kim Hye-Soo
Han Byung-Hoon
Kim Sun-Jung
Lee Jee-Sook
Park Sae-Jin
Lee Sang-Uk
Huh Bang
Kim Jeong-Hyun
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Abstract
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Rare autosomal dominant disorders associated with various tumors and cysts, and several kinds of pancreatic lesions have been described in patients with von Hippel- Lindau (VHL) disease, but there have been few studies concerned with the variations of the pancreatic duct. We experienced a case of pancreatic dual Wirsung ducts in a patient with VHL disease. Computed tomography scans showed that multiple cysts had nearly completely replaced the pancreas, there was a solid tumor on the uncinate process of the pancreas and a left renal mass suggested renal cell carcinoma. ERCP shows that the Santorini duct and Wirsung duct were fused in a normal fashion, and another Wirsung duct had shrub-like branches that are commonly seen in pancreatic divisum.
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KEYWORD
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von Hippel-Lindau disease, Pancreas, Pancreatic duct, Dual Wirsung ducts
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